- •The aim was to evaluate scoliosis onset and progression in untreated type II SMA patients.
- •The mean annual rate of increase of scoliosis angle was 5.63 (95%CI: 4.74–6.52).
- •The progression of scoliois angles was related to different variables.
- •Angles progressively increased with decreasing HFMSE scores or increasing age.
- •Our results confirm the progression of scoliosis in type II SMA.
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