Neuromuscular Disorders
Volume 19, Issue 6 , Pages 391-396 , June 2009

Increased fat mass and high incidence of overweight despite low body mass index in patients with spinal muscular atrophy

  • Douglas M. Sproule

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
    • Corresponding Author InformationCorresponding author. Tel.: +1 212 342 6858; fax: +1 212 305 1253.
  • ,
  • Jacqueline Montes

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
  • ,
  • Megan Montgomery

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
  • ,
  • Vanessa Battista

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
  • ,
  • Dorcas Koenigsberger

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
  • ,
  • Wei Shen

      Affiliations

    • The Obesity Research Center, St Luke’s–Roosevelt Hospital, New York, NY, USA
    • Institute of Human Nutrition, Columbia University College of Physicians and Surgeons, New York, NY, USA
  • ,
  • Mark Punyanitya

      Affiliations

    • The Obesity Research Center, St Luke’s–Roosevelt Hospital, New York, NY, USA
  • ,
  • Darryl C. De Vivo

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA
  • ,
  • Petra Kaufmann

      Affiliations

    • Division of Pediatric Neurosciences, Department of Neurology, SMA Clinical Research Center, Columbia University Medical Center, Harkness Pavilion, HP-514, 180 Fort Washington Avenue, New York, NY 10032-3791, USA

Received 29 November 2008 ,Revised 9 March 2009 ,Accepted 27 March 2009.

References 

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PII: S0960-8966(09)00087-X

doi: 10.1016/j.nmd.2009.03.009

Neuromuscular Disorders
Volume 19, Issue 6 , Pages 391-396 , June 2009